MTE #20: Congenital Portosystemic Shunts—Diagnosis and Management (Ticketed)

Congenital portosystemic shunts (CPSSs) are an underdiagnosed vascular malformation causing portomesenteric blood to partially or completely bypass the liver. These shunts are associated with a wide spectrum of clinical manifestations, some of which are life threatening such as portopulmonary hypertension and liver malignancies. Additionally, persons with CPSS may present with renal, endocrine, or neurologic signs and symptoms. Diagnostic delay is common owing to the nonspecific presentation. The Pediatric Special Interest Group presents this expert session that utilizes an informal, small-group forum for in-depth discussion of CPSS with recognized leaders in pediatric hepatology and surgery, and interventional radiology. Presenters explore real-world challenges faced by clinicians tackling the management of complex patients with CPSS. Topics include management of the multiple clinical manifestations associated with CPSS, how and when to close shunts, and long-term follow-up. The session equips attendees with the tools necessary to ensure safe and effective management of patients with CPSS to improve long-term outcomes.