Biliary apotopes and anti‐mitochondrial antibodies activate innate immune responses in primary biliary cirrhosis
Ana Lleo, Christopher L. Bowlus, Guo‐Xiang Yang, Pietro Invernizzi, Mauro Podda, Judy Van de Water, Aftab A. Ansari, Ross L. Coppel, Howard J. Worman, Gregory J. Gores, M. Eric Gershwin – 26 August 2010 – Our understanding of primary biliary cirrhosis (PBC) has been significantly enhanced by the rigorous dissection of the multilineage T and B cell response against the immunodominant mitochondrial autoantigen, the E2 component of the pyruvate dehydrogenase complex (PDC‐E2). PDC‐E2 is a ubiquitous protein present in mitochondria of nucleated cells.