Caroli's disease and outcomes after liver transplantation
Farida Millwala, Dorry L. Segev, Paul J. Thuluvath – 27 December 2007 – Caroli's disease is a rare autosomal recessive disorder characterized by intrahepatic cystic dilatation of the bile ducts that, when progressive, leads to intrahepatic stones, recurrent cholangitis, portal hypertension, cholangiocarcinoma, and liver failure. Liver transplantation is a promising curative option for advanced Caroli's disease.