Rapid evolution of congenital hepatic fibrosis after liver transplantation for acute liver failure: The potential role of extrahepatic factors
Judith Flores, Ronen Arnon, Raffaella A. Morotti, Lisa Guay‐Woodford, Sukru Emre, Benjamin L. Shneider – 23 April 2008 – A 9‐year‐old male underwent deceased donor liver transplantation for idiopathic fulminant hepatic failure. In the postoperative period, a review of perioperative biopsies of the donor liver revealed mild features of congenital hepatic fibrosis. Over the ensuing year, the recipient developed severe complications of congenital hepatic fibrosis including multiple episodes of cholangitis and progressive portal hypertension.